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Biomedical subjects

J J Baudon

Publications and source records attributed to J J Baudon.

At least 37 records · Page 2Linked to original sources
PubMed1991

Renovascular hypertension: a rare cause of neonatal salt loss.

We report a case of severe hypertension in the newborn period due to obstruction of the right renal artery. The baby presented with polyuria leading to dehydration and was found to have hyponatraemia and severe renal salt loss. When sudden malignant hypertension is induced in experimental conditions, a high pressure diuresis and increased angiotensin II production are found. These findings could explain the renal salt loss, notwithstanding the effects of secondary hyperaldosteronism and hyper-reninaemia.

Dehydration↗
PubMed1991

[Severe rumination in infants].

Rumination or merycism is a rare but potentially life-threatening condition. Six boys, aged 5 to 14 months, were hospitalized for growth retardation (-2 to -4 SD) and vomiting. In 5 of 6, mothers noticed the vomiting but not rumination. Diagnosis was based on clinical observation only. No significant abnormalities were found by other investigations. A short nutritional rehabilitation followed by mothering performed by the nurses resulted in a weight gain of 1 to 2.3 kg over the next 15 to 90 days. Rumination results from an affective deficiency of the infant and his mother as well. It appears as a destructive autoerotic reaction whose basis is depressive. Characteristic of the infant's recovering stage is a holding response when taken in the arms. However, various psychological perturbations persist after treatment.

Gastroesophageal Reflux↗
PubMed1989

Beckwith-wiedemann syndrome and neural crest tumors. A report of two cases.

We report 2 cases of thoracic neural crest tumors complicating the course in patients with Beckwith-Wiedemann syndrome (BWS). In the first patient, a thoracic neuroblastoma was fortuitously discovered at age 3 months on a chest film prior to a partial glossectomy. In the follow-up left nephroblastoma and a right kidney simple cyst appeared. In the second patient, a thoracic tumor which proved to be a mature ganglioneuroma was discovered at age 4 years on a follow up spinal radiograph. Although less frequent than nephroblastoma and/or adrenal tumors, the occurrence of thoracic neuroblastoma in BWS suggests that periodic chest radiograph and assays of HVA, VMA and Dopamine should be included in the follow-up protocol.

Beckwith-Wiedemann Syndrome↗
PubMed1987

Sclerosing cholangitis with neonatal onset.

Sclerosing cholangitis is characterized by irregular narrowing of extrahepatic or intrahepatic bile ducts, and in adults is defined mainly by radiologic findings. We describe eight children with cholestasis from the first week of life, followed by early cirrhosis and portal hypertension. Histologic examination of the liver showed absence of interlobular bile ducts in the early cholestatic phase in two patients and biliary cirrhosis later in all patients. Radiologic examination by percutaneous cholecystography under ultrasound guidance, carried out at age 8 months to 9 years, disclosed abnormal intrahepatic bile ducts with rarefaction of segmental branches, stenosis, and focal dilation. The extrahepatic ducts were involved in six patients. No intestinal disease has been found in these patients.

Bile Ducts↗
PubMed1982

[Global pancreatic and gastric deficiency after a familial membranous glomerulonephritis in a child treated by corticoids and chlorambucil for a long time (author's transl)].

A 2-year-old boy with familial extramembranous glomerulonephritis was unfortunately treated with corticosteroids (1 to 0.5 mg/kg/day) and Chlorambucil (cumulative dose: 2.5 g) over a period of 7 years. Three years later, after recovery from the renal affection, he developed fatty diarrhoea from exocrine pancreatic deficiency, followed 5 years later by the onset of diabetes with hypochlorhydric gastritis. The diagnosis of non-calcifying chronic pancreatitis was suggested by scintigraphic and ultrasonographic investigations and confirmed by the marked increase in lactoferrin levels and the lactoferrin/lipase ratio (greater 0.1 p. cent) in pancreatic juice. The etiology was more likely to be direct toxicity of corticoids and/or immunosuppressors on the pancreas than an immunologically-mediated disease.

Adolescent↗
PubMed1980

Uropathies diagnosed in the neonatal period: symptomatology and course.

Forty infants with a uropathy diagnosed during the first two months of life were studied. Presenting signs were urinary tract infection in one-half of the cases, disorders of micturition, pelvic or abdominal wall malformations, abdomino-pelvic mass, and macroscopic hematuria. Obstructive uropathy was observed in 17 children and vesicoureteric reflux in 29. We noted a high incidence of extrarenal malformations (14 of the 40 cases) in this series of uropathies diagnosed during the neonatal period. Despite early diagnosis, the course was not favorable in 11 cases with congenital anomalies of the renal parenchyma.

Female↗
PubMed1978

[Acrodermatitis enteropathica. Anatomo-clinical study of 2 familial cases treated with zinc sulfate].

Two familial cases of acrodermatitis enteropathica began at the time of weaning, with characteristic dermatologic lesions and digestive signs, resulting in lack of weight gain: at 13 months of age growth future was evident in the elder child. The anatomic lesions were those of an exophagitis and, in the duodenal mucosa, a dilation of the capillaries of the chorion in the absence of villous atrophy. The ultrastructural study showed inclusions in Paneth's cells, and changes in keratin cells, with intra-cytoplasmic vacuoles and abnormal melanin pigment in the skin. The administration of zinc sulphate induced a rapid recovery of cutaneous lesions and resumption of growth. The interruption of treatment resulted twice in a quite immediate relapse of cutaneous signs in the first patient, which was rapidly reversible with the reintroduction of zinc sulphate.

Acrodermatitis↗