Search PubMed⌕ Search

SEARCH · Search PubMed

Results for “Tracheobronchomegaly”

Search indexed PubMed citations on genomics, clinical trials, systematic reviews and public health. Explore titles, authors and supplied subject terms, then open the PubMed record.

Quote a phrase for an exact phrase match. Source license links do not imply unrestricted reuse.

At least 19 recordsLinked to original sources
PubMed2000

Recurrent lower respiratory tract infections in a 14-year-old boy with tracheobronchomegaly (Mounier-Kuhn syndrome).

Tracheobronchomegaly (Mounier-Kuhn syndrome) is characterized by dilatation of the central airways, tracheobronchial outpouchings, and chronic tracheobronchitis. Most cases are diagnosed in adulthood. We report the clinical, radiographic, and bronchoscopic findings in a 14-year-old boy with tracheobronchomegaly, ptosis of the right eyelid, and redundant skin and mucosa of the upper lip, who presented with a 2-year history of recurrent lower respiratory tract infections. Pediatricians should be aware of the possibility that tracheobronchomegaly may cause clinical symptoms in childhood and adolescence. Pediatr Pulmonol. 2000; 29: 476-479.

Adolescent↗
PubMed2002

[Treatment of tracheobronchomegaly with an Ultraflex prosthesis. A case report].

Tracheobronchomegaly is defined as a dilatation of the trachea and the large bronchi. It may occur as a familial condition or in association with a connective tissue disease, e.g. Ehlers-Danlos syndrome. Tracheobronchomegaly occurs late in adults. The predominant symptoms are bronchial irritation and recurrent bronchopulmonary infections (because of ineffective cough). Diagnosis is provided by thoracic imaging, particularly computed tomography that enables measuring the precise diameter of the trachea. We report the case of one patient with tracheobronchomegaly who was greatly improved after implantation of Ultraflex tracheobronchial prostheses.

Diagnosis, Differential↗
PubMed1995

[Tracheobronchomegaly (Mounier-Kuhn syndrome): roentgen findings and tracheal stent instrumentation].

Tracheobronchomegaly is a rare disorder of the lower respiratory tract characterised by marked dilatation of the trachea and the central bronchi associated with recurrent respiratory tract infections. However, some patients with tracheobronchomegaly are not detected because the symptoms are overlooked if chest radiographs alone are used for diagnosis. We encountered two cases of tracheobronchomegaly that were not diagnosed by chest radiographic examinations but were shown clearly with CT. We believe that patients with recurrent pulmonary infection must be examined with the use of CT.

Aged↗
PubMed1997

[Tracheobronchomegaly--Mounier-Kuhn syndrome--case report and review of the literature].

Tracheobronchomegaly is a rare disorder. A marked dilatation of the trachea and the main stem bronchi is the characteristic sign measured as an enlarged transverse diameter (mean +/- 3 SD). Bronchiectasis is usual. In about one third of the published cases a diverticulosis was described as demonstrated in one our cases. For diagnostic modern radiological methods (CT including 3 D reconstruction, MRT) and bronchoscopy are recommended. The number and seize of the diverticula are documented by tracheography or by bronchography. In a part of all cases of tracheobronchomegaly the cause of the disorder is known. Therefore a division into congenital and acquired tracheobronchomegaly is useful.

Aged↗
PubMed1987

Neonatal tracheobronchomegaly.

Tracheobronchomegaly is rarely reported in neonates. We present five cases of tracheobronchomegaly occurring in neonates receiving intensive ventilatory and oxygen support. Barotrauma is speculated to be the primary pathophysiologic factor in these cases.

Diseases in Twins↗
PubMed1995

Anaesthesia for a patient with tracheobronchomegaly (Mounier-Kuhn syndrome).

Tracheobronchomegaly is a rare condition in which anaesthetic experience is limited. Patients with tracheobronchomegaly are at risk of large airway collapse and obstruction, aspiration pneumonitis and tracheal trauma following airway instrumentation. We describe our anaesthetic technique and problems encountered during nephrectomy in a patient with this condition.

Aged↗
PubMed1990

Acquired tracheobronchomegaly resulting in severe respiratory failure.

Tracheobronchomegaly is a distinct clinical and radiologic entity characterized by marked dilatation of the trachea and bronchi. In this report we describe a Marfanoid patient who developed TBM in his adulthood with rapid deterioration, leading to hypercapnic respiratory failure. This case represents an acquired form of TBM in a patient with Marfanoid features which has not been previously described. Tracheobronchomegaly should be considered as a cause of chronic respiratory failure in a young adult and can be diagnosed easily with chest roentgenogram and CAT scan.

Adult↗
PubMed1994

Tracheobronchomegaly accompanied by bilateral giant pulmonary bullae and left spontaneous pneumothorax. Case report.

A 58-year-old man with tracheobronchomegaly underwent simultaneous bilateral pulmonary surgery via median sternotomy for left spontaneous pneumothorax with bilateral giant bullae. Postoperative hypoxaemia and pneumonia necessitated ventilator and antibiotic treatment. Simultaneous bilateral pulmonary operations in patients with tracheobronchomegaly carry a risk of respiratory complications.

Humans↗
PubMed2000

[A case of tracheobronchomegaly].

We report a rare case of tracheobronchomegaly with crescent-type tracheobronchomalacia. A 77-year-old man with a chronic cough was referred to our hospital because of fever and dyspnea. Radiographic examination showed enlargement of the trachea and main bronchi. On chest radiography, the transverse diameter of the trachea was 31 mm, and consolidation shadows were seen in both upper lung fields. Tracheobronchomegaly with pneumonia was diagnosed. The pneumonia was improved by administration of PAPM/BP. On bronchoscopic examination, the trachea and main bronchi were extremely dilated on inspiration, and were collapsed on expiration. The biopsy specimen from the bronchial mucosa showed non-specific chronic inflammation.

Aged↗
PubMed2002

[Laryngeal carcinoma associated with congenital tracheobronchomegaly (Mounier-Kuhn syndrome): a case report].

Congenital tracheobronchomegaly or Mounier-Kuhn Syndrome is a rare disorder of controversial etiology. It is characterized by an abnormal enlargement of the trachea and primary bronchi, because of atrophy or absence of their elastic fibers and smooth muscles. Such alterations lead to the collapse of the respiratory tract during forced exhalation, making expectoration by coughing of little use. Subjects with this disorder are, therefore, predisposed to the development of phlogistic bronchopulmonary pathologies such as bronchitis, emphysema, bronchiectasis and pulmonary fibrosis. The present work reports the case of a 65-year-old man suffering from asymptomatic congenital tracheobronchomegaly which was unknown until preoperative testing was performed (standard chest x-ray, tracheobronchoscopy) following a diagnosis of squamous cell carcinoma of the larynx. The patient underwent total laryngectomy and bilateral neck dissection without any intra- and postoperative complication. This is the first case reported in the literature of an association between laryngeal carcinoma and Mounier-Kuhn Syndrome, although a cause-effect relationship between the two pathologies cannot be advanced at this time. This paper also reports how the patient was managed in terms of anesthesiology and surgical technique, both conditioned by the marked tendency for anteroposterior tracheal wall collapse and its high reactivity to mechanical insults.

Aged↗
PubMed1995

Tracheobronchomegaly in preterm infants on mechanical ventilation.

Tracheobronchomegaly (TBM) was diagnosed on chest radiographs as an apparent dilatation of the trachea and main bronchi in four premature infants on prolonged mechanical ventilation for respiratory distress syndrome. In a retrospective study, the parameters of assisted ventilation, the Apgar score, the presence of conatal or later infection, and hypotension were reviewed and analyzed as factors possibly contributing to the pathogenesis of TBM in these infants. The results lead to the conclusion that TBM in premature infants on prolonged ventilatory support is an acquired condition though a congenital defect cannot be excluded as a probable predisposing factor. In the etiopathogenesis of TBM, a repeated barotrauma of prolonged ventilation is a crucial factor while the severity of lung disease and the degree of prematurity, hypotension, infection, and generally poor clinical condition, all appear to be relevant in the development of TBM in a premature infant with respiratory distress syndrome.

Apgar Score↗
PubMedDate not supplied

Tracheobronchomegaly: clinical aspects and radiological features.

Tracheobronchomegaly is a rare--probably congenital--disorder. Its clinical appearance is non-specific. The diagnosis is made by radiological methods. This paper describes the typical features in early and advanced stages and outlines the diagnostic approach.

Adult↗
PubMed1991

Tracheobronchomegaly in association with ankylosing spondylitis.

We present a case of tracheobronchomegaly seen in association with ankylosing spondylitis. To the authors' knowledge this combination has not been previously described. A review of the chest radiographs of 30 other patients with ankylosing spondylitis revealed no evidence of tracheal dilatation.

Adult↗
PubMed2000

[Tracheobronchomegaly: an exceptional predisposing factor for pulmonary aspergillomas and massive hemoptysis].

Mounier-Kuhn syndrome--or tracheobronchomegaly--is a rare congenital disorder characterized by significant dilation of the trachea and main bronchi. It is accompanied by ineffective cough and is often complicated by recurrent lung infections and bronchiectasis. Clinical presentation varies widely, ranging from forms with scarce involvement of functional capacity to others that progress to respiratory failure that can prove fatal. We report an exceptional case of massive hemoptysis secondary to the presence of pulmonary aspergillomas and bilateral bronchiectasis in which bronchial arteriography with embolization and surgical resection were insufficient for resolving the complications.

Acute Disease↗
PubMed1994

[Tracheobronchomegaly associated with light chain deposition disease].

Tracheobronchomegaly, also known as Mounier-Kühn's Syndrome, is characterized by market dilation of the trachea and main bronchi and has been reported in association with several conditions, particularly connective tissue disease. The pathogenesis and clinical signs of light chain deposition disease are similar to those of light chain amyloidosis, in which these chains are deposited as amorphous material lacking the tinctorial features of the amyloid. We present a case involving both entities, an association that has not been previously reported, and we review the main characteristics of both diseases.

Aged↗
PubMedDate not supplied

CT features of tracheobronchomegaly.

This paper describes the appearance of tracheobronchomegaly (also termed Mounier-Kuhn syndrome) as demonstrated on CT in three patients. Features include dilatation of the trachea and mainstem bronchi, tracheal diverticulosis, bronchiectasis, and chronic pulmonary parenchymal disease.

Adult↗
PubMed1994

Tracheobronchomegaly: an unusual presentation of a rare condition.

Tracheobronchomegaly is a rare cause of recurrent chest infections often with persistent, unproductive cough. A case is described which presented as a severe life threatening pneumonia in which the bronchoscopic, radiographic, and computed tomographic findings are given.

Bronchi↗
PubMed1991

Tracheobronchomegaly associated with interstitial pulmonary fibrosis.

Tracheobronchomegaly (TBM) is the syndrome of enlarged trachea and main bronchi associated with recurrent and chronic respiratory tract infections. A 42-year-old man with TBM and diffuse interstitial pulmonary fibrosis is described. The possible relationship between the two entities is discussed and the etiology, pathogenesis, clinical manifestations, prognosis and treatment of TBM are reviewed.

Adult↗