Ectopia lentis in systemic heritable disorders.
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Oculoauriculovertebral dysplasia is a developmental disorder characterized by a triad of anomalies; epibulbar dermoids with or without lipodermoids, preauricular appendages or blind preauricular fistulae, and vertebral anomalies. Multiple associated anomalies have been reported. A case of this syndrome and a review of the literature are presented herein.
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