Search PubMed⌕ Search

SEARCH · Search PubMed

Results for “Cor Triatriatum”

Search indexed PubMed citations on genomics, clinical trials, systematic reviews and public health. Explore titles, authors and supplied subject terms, then open the PubMed record.

Quote a phrase for an exact phrase match. Source license links do not imply unrestricted reuse.

At least 91 records · Page 5Linked to original sources
PubMed1981

Cor triatriatum (subdivided left atrium).

Twenty-one patients (age 1 day to 156 months) with cor triatriatum sinister (subdivided left atrium) were treated over a 23 year period at two institutions. Anatomic classification of the hearts revealed 20 (95%) with classical cor triatriatum and normal pulmonary venous connections. One other patient had partial anomalous pulmonary venous connection. Three of these patients (14%) had other severe associated cardiac anomalies. Surgical correction of isolated cor triatriatum was performed in 13 patients of whom eight (62%) survived. Long-term results were excellent in seven (88%) patients; one late death occurred. A right atrial approach for infants and small children is recommended, while the left atrial approach appears satisfactory for larger children.

Adolescent↗
PubMed1995

Cor triatriatum: report of an unusual variant--triatrial heart. A case report.

Cor triatriatum is a rare cardiac malformation presenting with symptoms and signs of pulmonary venous obstruction. Although diagnosis of this defect has been facilitated by diagnostic procedures such as echocardiography and angiocardiography, it could be missed preoperatively. The authors report a case of cor triatriatum that is unique in having two separate atrial septal defects in each side of the fibromuscular membrane and that was undiagnosed preoperatively with transthoracic echocardiography and cardiac catheterization.

Child, Preschool↗
PubMedDate not supplied

[Doppler echocardiography in cor triatriatum: apropos of 2 cases].

In this communication we present a Doppler-echocardiographic investigation on two cases of cor triatriatum. The echocardiographic features and the pulsed Doppler findings, which have not been published previously, are also discussed. When the Doppler sample volume is positioned in the distal camera of the left atrium from apical projections, a positive systolic flow is obtained. This finding has not been described, to our knowledge, in the cor triatriatum nor in any other cardiac abnormality. It is our thought that flow studies in the left atrium in cases of cor triatriatum can be a useful aid to the echocardiographic diagnosis of the anomaly. Doppler studies are also helpful in the differential diagnosis with other intracavitary images, and it is probably also useful in the assessment of the degree of obstruction at the membrane level.

Adult↗
PubMed1990

Cor triatriatum dexter: antemortem diagnosis in an adult by cross sectional echocardiography.

Cor triatriatum dexter is a rare cardiac abnormality in which the right atrium is subdivided into two distinct chambers. This anomaly is generally attributed to the persistence of the right sinus venosus valve and it is frequently associated with severe malformations of other right heart structures. The antemortem diagnosis of the membrane may be difficult and its presence is often only established at necropsy. In a woman of 56 with Ebstein's anomaly the echocardiographic features of cor triatriatum dexter were examined before and during cardiac catheterisation. These investigations showed the position of the membrane, that there was no gradient between the two atrial chambers, and that there were perforations in the centre of the membrane.

Cor Triatriatum↗
PubMed1979

COMPLETE ATRIOVENTRICULAR CANAL AND COR TRIATRIATUM.

Two patients with complete atrioventricular canal and coexisting cor triatriatum are described. This rare combination of defects probably results from nonrelated embryological events. Successful correction was limited by the major lesion, complete atrioventricular canal, due to inadequate reconstruction of the atrioventricular valve. The associated cor triatriatum, which had not been identified prior to surgery, presented difficulties during operation.

Journal Article↗
PubMed2002

Maze procedure and cor triatriatum repair.

A 39-year-old man had cor triatriatum (Lucas-Schmidt type IA) with severe mitral regurgitation and atrial fibrillation. We performed resection of the anomalous septum between the accessory chamber and the left atrium, and conducted mitral valve repair and the maze procedure. The patient regained sinus rhythm and normal pulmonary venous drainage to the left ventricle without mitral regurgitation. Histological examination demonstrated fibrotic myocardial structures in the anomalous septum. The maze procedure and complete excision of the anomalous septum proved to be effective surgical treatment for atrial fibrillation with cor triatriatum.

Adult↗
PubMed1988

Magnetic resonance imaging of cor triatriatum.

Magnetic resonance imaging utilizing spin echo sequences was used to demonstrate cor triatriatum in an 18-year-old boy. Phase map images aided the diagnosis by demonstrating the presence of slowly flowing blood in the accessory atrial chamber. Magnetic resonance is an excellent modality for the noninvasive diagnosis of cor triatriatum.

Adolescent↗
PubMed1987

Cor triatriatum associated with partial anomalous pulmonary venous connection to the coronary sinus: echocardiographic and angiocardiographic features.

An infant girl is described who had cor triatriatum and partial anomalous pulmonary venous connection of the left pulmonary veins to the coronary sinus, the first report of this combination of lesions. The infant also had a Dandy-Walker malformation and multiple facial and intrathoracic hemangiomas. The cardiac diagnosis was made by two-dimensional echocardiography. Cardiac catheterization and angiography confirmed the findings and also demonstrated a persistent left superior vena cava draining to the coronary sinus. The infant underwent successful surgical repair. Partial anomalous pulmonary venous connection and left superior vena cava not infrequently are associated with cor triatriatum. Although two-dimensional echocardiography is sensitive for the detection of cor triatriatum, preoperative cardiac catheterization is necessary to identify unequivocally systemic and pulmonary venous connections.

Angiocardiography↗
PubMed1992

[Cor triatriatum in adulthood: Doppler echocardiographic diagnosis. Case report of an asymptomatic adult].

Cor triatriatum is a rare cardiac malformation occurring in about 0.1% of all congenital heart disease. As symptoms are usually present soon after birth, diagnosis in adulthood is extremely rare. We describe a case of a 33-year-old asymptomatic woman who was referred for echocardiographic examination because of a postural variable systolic click. The anatomy of the malformation and the hemodynamics of the left atrium were accurately assessed by means of conventional transthoracic Doppler echocardiography. The antero-inferior course of the intraatrial membrane inserting proximal to the left atrial appendage was documented in multiple perpendicular planes of examination. All pulmonary veins drained correctly into the proximal compartment of the left atrium. Additionally, a small atrial septal defect communicated between the distal compartment of the left atrium and the right atrium. Using pulsed wave Doppler, no site of pressure gradient could be detected between the two compartments of the left atrium. Thus, conventional transthoracic Doppler echocardiography represents an adequate tool for assessing cor triatriatum in adults. The patient refused transesophageal echocardiography.

Adult↗
PubMed1990

Cor triatriatum: clinical presentation and surgical results in 12 patients.

Twelve patients with cor triatriatum have been seen at our institution since 1979. The clinical presentation, diagnostic evaluation, and surgical results are outlined in this retrospective review. Operation is the treatment of choice for this rare congenital cardiac defect. One patient died 1 day before scheduled operation, and 2 patients died postoperatively, yielding a surgical mortality rate of 17% and an overall mortality rate of 25%. Resection of the obstructing atrial membrane was performed using hypothermic cardiopulmonary bypass in all cases. Left atriotomy was performed in 6 patients, and right atriotomy was performed in 7. The two postoperative deaths occurred in patients who had serious associated cardiac defects. Associated anomalies include atrial septal defect, persistent left superior vena cava, and partial anomalous pulmonary venous return. The postoperative course has been excellent in all 9 surviving patients; all remain asymptomatic. Cor triatriatum is amenable to surgical repair with excellent results when diagnosed early and when not complicated by other severe cardiac anomalies.

Child, Preschool↗
PubMed2004

Cor-triatriatum sinister presenting in the adult as mitral stenosis: an analysis of factors which may be relevant in late presentation.

BACKGROUND: Cor-triatriatum sinister is a rare congenital heart defect resulting from the division of the left atrium by a fibro-muscular membrane. It is usual for patients to present in infancy and early childhood, although some cases remain undetected until adult life. As a consequence of trans-membrane flow obstruction, the clinical features often mimic mitral stenosis. At present, the reasons for late presentation are poorly understood. METHODS: A complete review of all cases of cor-triatriatum sinister published in the English literature from 1966 to date as mitral stenosis was performed. Statistical analysis was carried out to determine associations between measurements reflecting the communicating membrane fenestration area, the presence of several clinical variables and patient age at initial presentation. RESULTS: Both pulmonary capillary wedge pressure and mean pressure gradient were significantly higher in younger adults. In addition, the incidence of atrial fibrillation and mitral regurgitation was found to rise with advancing age. CONCLUSIONS: Cor-triatriatum sinister remains an uncommon form of congenital heart disease although it is being diagnosed with increasing frequency in adults due to improvements in diagnostic imaging. This diagnosis should be considered in all patients presenting with signs or symptoms of mitral stenosis.

Adult↗
PubMed1987

Cor triatriatum dexter: two-dimensional echocardiographic diagnosis.

Cor triatriatum dexter is a malformation resulting from lack of normal regression of the embryonic right valve of the sinus venosus. In this situation, the right atrium is divided by a membrane into two chambers. Two-dimensional echocardiography was used in the antemortem diagnosis of this rare cardiac anomaly in a neonate. Associated cardiac lesions were also documented. The patient died, and findings were verified at autopsy.

Abnormalities, Multiple↗
PubMed1989

[Surgical experiences of Cor triatriatum in infancy].

Three operative cases with Cor triatriatum, age ranged from 30 days to 16 months, were presented. All types were IB1 of Lucas-Schmidt's classification and one patient was associated with right upper PAPVC. One patient died of low output syndrome due to preoperative shock. Communication of abnormal diaphragm in left atrium varied from small and multiple to 5 mm in diameter. Their preoperative diagnoses were established by two-dimensional echocardiogram prior to angiocardiogram and the intracardiac communications were well evaluated by color doppler echocardiogram which was superior to angiocardiogram in this evaluation. Postoperatively, no abnormal diaphragm were detected in two survivors. The diagnosis and operative procedure for this anomaly were discussed on.

Angiocardiography↗
PubMed2002

Use of Inoue balloon dilatation method for treatment of Cor triatriatum stenosis in a child.

An 8-year-old girl was referred for evaluation of a heart murmur and progressive dyspnea with exertion. Transthoracic echocardiogram revealed Cor triatriatum with severe stenosis at its orifice. The resting transmembrane CW Doppler velocity was 2.3 m/sec. Cardiac catheterization and hemodynamic assessment were performed and demonstrated a marked increase in pulmonary capillary wedge and pulmonary artery pressures. The stenosis was successfully dilated with an Inoue balloon using a transseptal technique. This is the first description of dilation of a Cor triatriatum using the Inoue technique. Only one previous case report of balloon dilatation for Cor triatriatum sinister has appeared in the English literature using a different technique (double balloon method).

Catheterization↗
PubMedDate not supplied

Operative correction of cor triatriatum sinister with systemic venous return anomaly (inferior vena cava-left atrium).

Cor triatriatum sinister is a rare cardiac anomaly. It is characterized by the presence of a fibromuscular membrane in the left atrium, thus forming a proximal chamber receiving the pulmonary veins and a distal chamber communicating with the mitral valve and the left atrial appendage. This rare pathology tends to coexist with a persistent left superior vena cava, whereas the presence of an anomalous systemic venous return is unusual. In this article, we report successful treatment of a patient with cor triatriatum sinister who has an additional systemic venous return anomaly.

Cardiac Surgical Procedures↗
PubMed1989

[Echocardiographic study of a cardiac murmur in cor triatriatum: a case report].

This is a report of an aged patient with cor triatriatum in whom the mechanism of his cardiac murmur was elucidated by Doppler and contrast echocardiography. This 63-year-old man was followed up for cardiomegaly detected at 40 years of age, and he had been treated for a cardiac murmur due to valvular disease during the previous 10 years. He was admitted to our hospital for the evaluation of incidental hematemesis. A phonocardiogram recorded over the apex showed a regurgitant murmur from early to mid-systole, followed by a continuous murmur lasting up to mid-diastole. Two-dimensional echocardiogram revealed an abnormal septum in the left atrium dividing the atrium into two chambers and showing bulging in late systole through diastole. In the lower chamber, color Doppler echocardiography disclosed continuous turbulent flow originating from the bulge directing the mitral orifice. Contrast medum coursing toward the mitral orifice was demonstrated during contrast echocardiography and left ventriculography, which coincided with the turbulent signal on the Doppler echocardiogram. The description of the cardiac murmur of cor triatriatum suggests that it is not persistent. Conceivably, it is a continuous murmur, whose mechanism can be elucidated by Doppler and contrast echocardiography.

Contrast Media↗
PubMed1986

Diagnostic features and pitfalls in the two-dimensional echocardiographic evaluation of a child with cor triatriatum.

Two-dimensional echocardiography has been successfully used to diagnose cor triatriatum in adults and children, and surgical referral of these patients has been undertaken without preceding cardiac catheterization and angiography. A child with cor triatriatum demonstrated by two-dimensional echocardiography was directly referred for surgical resection. Despite thorough preoperative echocardiographic examination and direct intraoperative inspection of the posterior left atrial chamber, partial anomalous right pulmonary venous drainage was not diagnosed until the postoperative period. The failure to detect this uncommon associated anomaly underscores the limitations of relying on two-dimensional echocardiography as the sole preoperative method of evaluation.

Echocardiography↗