Megalencephaly in the neonatal period as the initial manifestation of glutaric aciduria type I.
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Amino Acid Metabolism, Inborn Errors↗
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Acute pancreatitis in a patient with glutaric acidemia type I.
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Adult↗
The gem effect. I. The influence of 3-substituents on the rates of solvolysis of glutaric anhydride. A conformational analysis.
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Anhydrides↗
The gem effect. II. The influence of 3-mono- and 3,3-disubstitution on the rates of solvolysis of mono-p-bromophenyl glutarate.
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Chemical Phenomena↗
The gem effect. 3. The influence of 3-mono- and 3-gem substitution on the acid dissociation constants of glutaric acid. A comparison of the sensitivity of delta-pK-a of dicarboxylic acids and the rate of ring closure of their monoesters to the intramolecular distance separating carboxyl functions.
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Chemical Phenomena↗
A new class of hypocholesteremic agents: arylalkyl hydrogen succinates and glutarates.
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Anticholesteremic Agents↗
Synthesis and enantiomeric separation of 2-phthalimidino-glutaric acid analogues: potent inhibitors of tumor metastasis.
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Animals↗
Efficient synthesis of trisimidazole and glutaric acid bearing porphyrins: ligands for active-site models of bacterial nitric oxide reductase.
Ligands (1) for active-site models of bacterial nitric oxide reductase (NOR) have been efficiently synthesized. These compounds (1) feature three imidazolyl moieties and one carboxylic acid residue at the FeB site, which represent the closest available synthetic model ligands of NOR active center. The stereo conformations of these ligands are established on the basis of steric effects and 1H NMR chemical shifts under the ring current effect of the porphyrin.
Bacteria↗
Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.
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Adenosine Triphosphate↗
Clinically asymptomatic glutaric aciduria type I in a 4 5/12-year-old girl with bilateral temporal arachnoid cysts.
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Arachnoid Cysts↗
Feasibility of molecular prenatal diagnosis of glutaric aciduria type I in chorionic villi.
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Amino Acid Metabolism, Inborn Errors↗
Compound heterozygosity in the glutaryl-CoA dehydrogenase gene with R227P mutation in one allele is associated with no or very low free glutarate excretion.
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Alleles↗
Normal acylcarnitines in maternal urine during a pregnancy affected by glutaric aciduria type II.
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Acidosis, Renal Tubular↗
Biochemistry of glutaric aciduria type I: activities of in vitro expressed wild-type and mutant cDNA encoding human glutaryl-CoA dehydrogenase.
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Escherichia coli↗
Recurrent rhabdomyolysis in a child with glutaric aciduria type I.
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Child↗
3-Hydroxyglutaric and glutaric acids are neurotoxic through NMDA receptors in vitro.
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Animals↗
Evaluation of trigger factors of acute encephalopathy in glutaric aciduria type I: fever and tumour necrosis factor-alpha.
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Animals↗
A Korean girl with alpha-aminoadipic and alpha-ketoadipic aciduria accompanied with elevation of 2-hydroxyglutarate and glutarate.
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2-Aminoadipic Acid↗