Bicuspid aortic valve.
Bicuspid aortic valve is the most common congenital cardiac malformation and may be responsible for more mortality and morbidity than the combined effects of all the other congenital heart defects.
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Bicuspid aortic valve is the most common congenital cardiac malformation and may be responsible for more mortality and morbidity than the combined effects of all the other congenital heart defects.
Aortic regurgitation was the commonest functional anomaly among younger patients in a group of 63 individuals with a diagnosis of bicuspid aortic valve. With increasing age, a rise in the number with combined aortic valve disease and aortic stenosis was observed. Aortic dilatation was found in 65% of cases. Dilatation was independently associated with age and transvalvular aortic gradient.
The authors report a case of Brucella Melitensis endocarditis of a bicuspid aortic valve which caused rapid progression of the hemodynamic signs of aortic stenosis, and was associated with a para-aortic abscess and a pericardial effusion. Surgery resulted in correction of the hemodynamic abnormalities and cured the infection: the results were sustained 10 months after operation. This case illustrates the precision of the Doppler, echocardiographic diagnosis of the lesions, which was confirmed at surgery so that potentially dangerous cardiac catheterisation could be avoided.
Aortic valve insufficiency may occur in a number of backgrounds. A unique etiology is illustrated in a 53-year-old man with terminal cardiac failure due to ischemic heart and aortic valvular disease. Nodular calcification complicated a congenital bicuspid valve and caused erosion through a valve cusp, producing a chronic cusp defect and valvular insufficiency.
The present report describes a case of congenital bicuspid pulmonary valve which was observed in a male Japanese cadaver of 95 years old during dissecting practice at Gifu University in 1990. No evidence of heart failures was found. The semilunar valve on the left side was bigger than that of the right.
We report a rare case with a combination of cor-triatriatum, large secundum atrial septal defect and bicuspid aortic valve. The diagnosis was made by cross-sectional echocardiography. A defect was present between proximal (accessory) left atrial chamber and right atrium decompressing the accessory left atrial chamber. The large left to right shunt resulted in severe pulmonary arterial hypertension.
Calcified stenotic aortic valve are usually replaced by the artificial valve. Recently, we are trying to decalcify the calcification of the aortic valve by ultrasonic energy. This case report reviewed a small physique, 47 year old female, who had the calcified stenotic bicuspid aortic valve and the narrow aortic valve ring (18 mm diameter). The ultrasonic decalcification was performed by the ultrasonic surgical instrument, SUS-201D (ALOKA), ultrasonic energy output range from 25% to 45%. After the ultrasonic decalcification, the movability of the aortic cusps were improved and the aortic opening was enlarged. The systolic pressure gradient across the aortic valve was improved from 100 mmHg to 20 mmHg. This method "ultrasonic decalcification" is very useful technique for the repair of the calcified aortic valve stenosis.
The authors report a case of probable Haemophilus influenzae endocarditis in a 7 month-old infant with a bicuspid aortic valve. Precocity of the occurrence of endocarditis in such asymptomatic cardiac abnormality, scarcity of the suspected germ, and the observed mode of evolution are underlined. This case raises the problem of an endocardial involvement in an infant properly treated by adapted intravenous antibiotherapy. It can be concluded that regular clinical and echocardiographic examination is necessary for every case of severe Haemophilus influenzae infection.
Seven children with bi and 1 with tetracuspid aortal valve were examined. It was discovered that abnormalities of the aortal valves were associated with connective tissue dysplasias, hereditary syndromes and infectious endocarditis. The problem of bicuspid valve inheritance, prevalence and complications prophylaxis are under discussion.
We present the case of a 16 year old girl with the rare association of double mitral orifice and bicuspid aortic valve. The patient was asymptomatic and the defect was noted in two-dimensional echocardiographic examination. The clinical and therapeutical implications are discussed.
Among the gonadal dysgenesis, Turner's syndrome (T.S.) is often associated with cardiovascular malformations, mainly of the aorta. In order to assess noninvasively the incidence of those abnormalities we have evaluated 36 consecutive female patients (pts) with gonadal dysgenesis, mean age 13.3 +/- 2 years, range 3-24 years, without a prior history of cardiovascular disease, by clinical examination chromosomal karyotyping, 12 leads electrocardiography (ECG), and by Time Motion (TM) and Two-Dimensional (2D) Echocardiography (Echo). The following parameters were considered: presence of an auscultatory systolic ejection click (SEC); evidence of a bicuspid aortic valve (BAV); aortic valve stenosis (AVS); aortic valve eccentricity index (AVEI); left ventricle wall hypertrophy (LVWH). 9 pts out 36 (25%) presented a BAV at the 2D Echo; 8 pts out of 36 (22%) presented a SEC, 3/9 (33%) mild AVS, 2/9 (22%) displayed AVEI on TM study and 3/9 (33%) had LVWH. These findings indicate that an isolated BAV is present in a high percentage of pts with gonadal dysgenesis, more than before suspected. Echocardiography shows to be particularly useful and reliable in the assessment of that abnormality.
Congenital bicuspid stenosis with left ventricular hypoplasia was diagnosed in a kitten. Clinical weakness, dyspnoea and marked cardiomegaly (X rays) were related to postmortem findings. The cardiomegaly had resulted from an enlargement of the left auricular appendage. It is supposed the cardiomegaly developed after the closing of the foramen ovale.
Gross examination was done of 186 hearts, principally from adults, for the nature of the aortic valve and the source of the posterior descending coronary artery (origin from the right coronary artery indicated as right dominance, origin from the left circumflex artery as left dominance). Exclusive of cases with coarctation of the aorta, the overall incidence of left coronary dominance in cases with congenital bicuspid aortic valves was 24.4%, while in cases with tricuspid aortic valves the incidence was 9.5%. There appears to be a greater tendency for left coronary arterial dominance in coarctation of the aorta than in the general population regardless of the type of the aortic valve.
Mitral valve prolapse (MVP) associated with congenital bicuspid aortic valve (CBAV) is an uncommon finding. In a study of 257 black patients with MVP, the author identified eight patients with associated CBAV. This paper discusses the association of the two lesions in relation to etiologic and surgical implications.
OBJECTIVE: To illustrate and describe a variant of the congenitally bicuspid aortic valve (BAV) in the context of previous reports of the morphology of BAVs. SETTING: Retrospective review of surgically excised aortic valves at The University of Ottawa Heart Institute in Ottawa, Ontario. DESIGN AND PATIENTS: The clinical, echocardiographic and pathological features of 17 cases with a variant of BAV were examined from patients who had valve replacements performed in the period from January 1, 1986 to December 31, 1992. MAIN RESULTS: A total of 865 patients had native aortic valve replacements during the study period and 291 patients had BAVs. One hundred and eighty-one patients were male (62%) (mean age 60 years) and 110 were female (38%) (mean age 64 years). There were 17 BAVs (6%) where either: the raphe was fenestrated so that only a thin fibrous band (or bands) joined the valve cusp to aortic wall-type A valves (seven cases); or a similar fibrous band (or bands) was seen, but was associated with other usual appearing raphal tissue--type B valves (10 cases). These patients included 15 males (mean age 63 years) and two females (mean age 63 years); they presented with dyspnea and/or angina. Distinction of the number of cusps with this variant was incorrect in six of nine transthoracic echocardiograms, and three of four transesophageal echocardiograms. CONCLUSION: This variant of BAV, with fenestrated raphe, is not well described in the literature, is difficult to diagnose clinically and may present in unusual ways.
A 59-year-old man who complained of palpitation was diagnosed as having a congenitally bicuspid aortic valve, severe aortic regurgitation, and an ascending aortic aneurysm. He underwent aortic valve replacement and conduit replacement by the modified Wheat technique. Since this technique requires no coronary artery anastomosis, it causes no problems associated with reconstruction of the coronary artery. Postoperative angiogram revealed no aneurysm formation of the aortic root or paravalvular leakage. This case suggest that aneurysm of the ascending aorta with aortic regurgitation is more effectively treated by the modified Wheat technique if cephalad displacement of the coronary ostium is not extensive.
A 62-year-old female who had a complaint of palpitation was diagnosed as bicuspid aortic stenosis and left single coronary artery by the echocardiographic examination, cardiac catheterization study and coronary artery angiography. Aortic valve replacement was performed and the patient was discharged 22 days after surgery with good post-operative course. Preoperative coronary artery angiography was important in the case of aortic valvular disease.
Saccular aortic aneurysm arising in the ductal region, known as ductus diverticulum aneurysm, is a rare anomaly. Due to potentially malignant evolution, recognition of radiological signs associated with this anomaly during the asymptomatic phase may be important in order to plan surgical intervention in time. We report an unusual case of ductus diverticulum aneurysm combined with bicuspid aortic valve, dilatation of ascending aorta, and coronary artery disease.