Search PubMed⌕ Search

SEARCH · Search PubMed

Results for “ENCEPHALOCELE”

Search indexed PubMed citations on genomics, clinical trials, systematic reviews and public health. Explore titles, authors and supplied subject terms, then open the PubMed record.

Quote a phrase for an exact phrase match. Source license links do not imply unrestricted reuse.

At least 181 records · Page 10Linked to original sources
PubMed2000

[Spontaneous temporo-sphenoidal encephalocele. A case report].

A case of anteromedial temporo-sphenoidal meningo-encephalocele in a 43-year-old woman is reported. She was referred to us after a five-year history of rhinorrhea of CSF. Three years ago, she presented an epileptic seizure. CT scan showed an empty sella and an opacity of the right part of the sphenoid sinus. On coronal sections, a defect was visible in the superior wall of the right lateral recess of the sphenoid sinus. The lateral sphenoidal rhinorrhea was confirmed by a CT cisternography. The patient was operated on via a frontotemporal approach with an orbitozygomatic removal. The dural defect was filled by a patch of pericranium. The patient is without evidence of cerebrospinal fluid leak 2.5 years later. Fifteen cases of anteromedial temporosphenoidal meningo-encephaloceles have been reported. They probably are of a developmental origin. Some cases have been successfully treated via a transsphenoidal route. However, surgical failures related to this approach can be due to the lack of control of the lateral recess of the sphenoid sinus. Therefore, the frontotemporal approach seems more adequate.

Adult↗
PubMed2002

Growing-fracture of the orbital roof with post-traumatic encephalocele in an adult patient. Case report.

Growing fractures are a rare entity, usually occurring in paediatric age. Localisation at the orbital region is even rarer. We report the case of a growing fracture of the orbital roof with post-traumatic encephalocele in an adult patient, the 1(st) similar case in adulthood at our knowledge. Clinical and neuroimaging aspects are described, underlining the role of MRI in displaying intraorbital encephalocele. Surgical treatment with relevant technical notes is discussed as well.

Aged↗
PubMed2003

[Spontaneous intrasphenoidal encephalocele. Report of two cases revealed by rhinorrhea].

We report two cases of spontaneous anteromedial temporo-sphenoidal meningo-encephalocele. The first patient was a 67-year-old man with a history of treated epiglotic cancer 6 years ago, was referred to us for CSF rhinorrhea. Lateral sphenoidal CSF fistula was confirmed by CT cisternography. Four lumbar taps were performed and rhinorrhea stopped for 2 years. At relapse of rhinorrhea, the patient was operated on via a subtemporal approach. The dural defect was filled by an intradural patch of pericranium. Four years later patient showed no evidence of cerebrospinal fluid leakage. The second patient was a 54-year-old woman referred to us after a one year history of CSF rhinorrhea. CT cisternography confirmed lateral sphenoidal CSF fistula. The patient was operated on via a subtemporal approach. The dural defect was filled by a patch of pericranium. Three years later the patient had no evidence of cerebrospinal fluid leakage. Twenty-one cases of anteromedial temporosphenoidal meningo-encephaloceles have been reported in the literature. They probably are of a developmental origin. Some cases have been successfully treated via a transsphenoidal route. However surgical failures related to this approach can be due to the lack of control of the lateral recess of the sphenoid sinus. Therefore, the frontotemporal approach seems more adequate but the transphenoidal endoscopic approach will probably be used in the future.

Aged↗
PubMed1976

[Diagnosis and therapy of the nasoethmoidal encephaloceles (author's transl)].

Two typical cases of nasoethmoidal encephaloceles with liquorrhoea, which were operated on by neurosurgeons, are demonstrated. In one case, polyposis of the nose had been operated on twice in childhood, due to the ignorance of the cause with the result of a liquorrhoea. The second patient showed recurrent meningitis with nasal liquorrhoea and turricephaly. The tentative diagnosis of a nasoethmoidal enceplaocele which was suspected by x-ray-tomography and radio-isotopetest could be certified by the aid of detail-angiography. The neurosurgical technique of intracranial, intradural resection of the encephalocele and closure of the liquor fistual with an acrylic flap is shown.

Adolescent↗
PubMed2003

Two-stage management of mega occipito-encephalocele.

We report three cases of large occipito-encephaloceles that were managed in the Neurosciences Unit, Hospital Universiti Sains Malaysia over the last 5 years. All patients had pre-operative MRI (magnetic resonance imaging) evolution and mapping of the sagittal sinus tract. The cerebrospinal fluid (CSF) of all three patients were initially diverted by means of ventricular shunt two weeks prior to shunt removal. The slow drainage of CSF prevented electrolyte and volume disturbances due to sudden decompression during their definitive occipital encephalocele operations. After 3 years follow-up, all these patients are progressing well.

Encephalocele↗
PubMed2004

Spontaneous bilateral intrasphenoidal lateral encephaloceles: CT and MRI findings.

Lateral intrasphenoidal encephaloceles are rare anomalies. We describe a unique case in which spontaneous bilateral intrasphenoidal lateral encephaloceles were discovered in a 53-year-old man during a work-up for cerebrospinal fluid leak. We discuss our clinical findings and the results of preoperative computed tomography and magnetic resonance imaging.

Cerebrospinal Fluid Rhinorrhea↗
PubMed1992

Intraoperative management of an infant with a nasofrontal encephalocele.

1. An encephalocele is a congenital malformation in which the structures of the central nervous system, in communication with cerebrospinal fluid pathways, herniate through a cranial defect. 2. Classification of encephaloceles depends on their anatomical location within the cranium, and the prognosis and treatment largely depend on the site of such defects. 3. Although the operation is delayed until the infant gains strength, early correction (within the first month) minimizes facial deformity, prevents further damage to brain tissue herniating through the defect, and increases the chance of normal binocular vision.

Encephalocele↗
PubMed1992

[Dermoid cyst of the anterior fontanelle in children: clinical significance and differentiation from encephalocele].

Dermoid cysts of the anterior fontanel present as a tumor lesion that tenses up when the child cries or strains. Their midline position in the skull, the fact that some of these cysts contain clear fluid and the presence of an underlying bone defect, lead the clinician to the erroneous diagnosis of encephalocele, for which they are sent for consultation. We report a series of five of these cysts (3 dermoid and 2 epidermoid) located over the anterior fontanel, remark on their clinical significance, and stress their differential diagnosis from encephalocele and from other tumor lesions of the anterior fontanel.

Adolescent↗
PubMed2006

[Association of occipital encephalocele with vesicoureteral reflux].

Occipital encephalocele was associated with vesicoureteral reflux and agenesis of the os coccygeum in a small-for-gestational age newborn girl. The symptoms did not correspond to any of the syndromes with encephalocele. The present observation and data of the literature suggest that the significance of vesicoureteral reflux in syndrome diagnosis is generally underestimated.

Abnormalities, Multiple↗
PubMed2006

Cephalopagus conjoined twins presented with encephalocele: diagnostic role of ultrafast MR imaging.

Conjoined twinning is a rare abnormality and cephalopagus is a very rare form of conjoined twins. We report a case of cephalopagus conjoined twins with encephalocele and omphalocele which diagnosed by ultrasonography and ultrafast magnetic resonance (MR) imaging at 24 weeks of the gestation. Ultrafast MR imaging can provide image quality superior to two dimensional ultrasonography and should be considered an adjunct to ultrasound for antenatal characterization of some anomalies. To the best of our knowledge, this is the first case of cephalopagus conjoined twins with encephalocele and omphalocele which diagnosed by ultrasound and ultrafast MR imaging.

Abortion, Induced↗
PubMed1990

Bilateral orbital encephaloceles. An unusual cause of exophthalmos.

We report a case of bilateral orbital encephaloceles associated with exophthalmos of the left eye. Orbital encephaloceles, especially bilateral ones, are very rare. The surgical approach to the repair of this defect and reasons for preferring a transcranial approach are described and discussed.

Encephalocele↗
PubMed1989

Contributory aspects of MRI in the evaluation of basal encephaloceles.

Basal encephaloceles are rare pathologies which belong to the now well-defined complex called median cleft face syndrome. This entity includes median craniofacial dysraphism associated to a varying degree with optic tract pathology, dysfunctioning of the hypothalamus-hypophysis axis, agenesis of the corpus callosum and basal encephalocele. The latter is that virtually constant element for which surgery is frequently requested. Owing to the large number of surgical failures (especially in the transsphenoidal type) medical imaging for the evaluation of malformative damages must be very accurate. Until recently, the techniques available, such as standard radiography, conventional tomography, gas encephalography, carotid arteriography and computerized tomography with or without metrizamide cisternography, were either too invasive or too inaccurate. MRI is the technique which provides the best images of prolapsed meninges, brain regions or ventricles, as well as of the anatomical rapport between the hypophysis, the optic tract and the limbic system.

Encephalocele↗
PubMed1988

[Basal encephalocele--a report of two cases and consideration of its pathogenetic classification].

The authors have experienced two cases of basal encephalocele without intra and extra cranial anomalies. We have reviewed previous reported cases and studied, from the view point of developmental pathology, reasons why these cases did not have associated anomalies. In this paper we will report our two cases of basal encephalocele and propose a new classification for it, based upon the developmental pathology of the basal part of the skull and associated anomalies. Case 1. A 32 year old male complained of continuous rhinorrhea for 8 months. Coronal CT scan demonstrated a defect of the right sphenoid and ethmoid bone, and a protrusion of isodensity mass, which was enhanced by administration of metrizamide in the subarachnoid space. During the operation, the protruded mass was removed, and the defects of bone and dura mater were repaired. Postoperative course was uneventful. Case 2. A 33 year old male was referred from the department of otology to the department of neurosurgery, because of rhinorrhea and the presence of brain tissue at the time of nasal operation 3 months before. Coronal CT scan revealed a defect of the left ethmoid bone and a protrusion of isodensity mass in it. RI cisternography clearly demonstrated the leakage of CSF through the left nasal cavity. During the operation, the protruded mass was removed and the bone and dura mater defects were repaired. Postoperative course was uneventful. The common findings of both cases are that they were diagnosed by accident in adulthood cases of rhinorrhea, and midsagittal basal bone structure was preserved without extra and intra cranial anomalies.(ABSTRACT TRUNCATED AT 250 WORDS)

Adult↗
PubMed1988

Intrasphenoidal encephalocele: report of a case.

The diagnosis of intrasphenoidal encephalocele may be difficult because of its rarity and its nonspecific signs and symptoms. The authors report a patient with intrasphenoidal encephalocele who was operated on by the transsphenoidal approach with a good result. They also review five reported cases, with discussion of their clinical characteristics and operative indications.

Encephalocele↗
PubMed1987

[Encephaloceles].

A 42-year-old woman presented with persistent headaches, vertigo, vomiting and transient periods of unconsciousness. Examination revealed a spheno-nasopharyngeal encephalocele lying between the ethmoid bone and the sphenoid sinus. It was possible to push the prolapse gently back by a transmaxillary procedure and to close the bony gap with resorbable cellulose. Long term follow up revealed no further complications and complete healing. The otorhinolaryngologist should be willing and able to treat such encephaloceles of the ethmoid roof or of the sphenoid sinus.

Adult↗
PubMed1986

Anterior encephalocele presenting as nasolacrimal obstruction.

A case of congenital anterior encephalocele presented originally with nasolacrimal obstruction. Associated paranasal masses and hypertelorism suggested the diagnosis, which was confirmed and delineated by computed tomography. Anterior encephalocele has various clinical presentations, but the diagnosis should be suspected in a child with nasolacrimal obstruction and associated congenital anomalies, particularly paranasal masses. Early recognition is essential to prevent trauma to CNS tissue, to prompt evaluation for other congenital anomalies, and to facilitate appropriate neurosurgical repair.

Child, Preschool↗
PubMed1986

Congenital meningocele-encephalocele in an experimental swine herd.

Fourteen instances of meningocele-encephalocele in an experimental herd were recorded over a 5-year period. Thirteen of these affected animals were subjected to extensive pedigree analyses. Familial associations were strong, and clearly the meningocele-encephalocele in this herd was under genetic influence. However, additional studies are needed to clarify the mode of inheritance and, perhaps, to identify other factors that might be involved.

Animals↗
PubMed1979

Occipital encephalocele with holoprosencephaly and aqueduct stenosis.

A case is described in which an occipital encephalocele was removed in a newborn and in which a midline monoventricle did not appear until some months later, suggesting the diagnosis of holoprosencephaly. The relationship of encephaloceles and holoprosencephaly is discussed.

Cerebral Aqueduct↗