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PubMed · 8858385

Autoimmune polyendocrinopathy--candidiasis--ectodermal dystrophy (APECED).

J Perheentupa
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Abstract

APECED, an autosomal recessive disease manifests itself as a widely variable combination of three groups of components: 1) autoimmune destruction of tissues, predominantly endocrine glands, 2) chronic superficial candidiasis, and 3) ectodermal dystrophy. Clinical and basic information obtained from Finnish series of 72 patients is reviewed.

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Addison DiseaseAdolescentAdultAutoimmunityCandidiasisChildChild, PreschoolDiabetes Mellitus, Type 1FemaleHumansHypoparathyroidismHypothyroidismIncidenceInfantMaleMiddle AgedPolyendocrinopathies, AutoimmuneJournal ArticleReview

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BibTeXRIS

J Perheentupa. 1996. Autoimmune polyendocrinopathy--candidiasis--ectodermal dystrophy (APECED).. https://doi.org/10.1055/s-2007-979814

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PubMed2006

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[Diagnostic image (303). A deeply tanned woman].

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