The porphyrias.

H A Werman

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PubMed · 2680472

The porphyrias.

H A Werman

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Abstract

The importance of recognizing these rare metabolic disorders in the Emergency Department patient is discussed. The pathophysiologic mechanisms behind the neurologic and cutaneous manifestations of these disorders is reviewed; presentation and management of the acute hepatic porphyrias are described; and features of the erythropoietic porphyrias and porphyria cutanea tarda are presented.

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Acute Disease Erythropoiesis Heme Humans Liver Diseases Porphyrias Skin Diseases Journal Article Review

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H A Werman. 1989. The porphyrias.. https://pubmed.ncbi.nlm.nih.gov/2680472/

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