[Red cell membrane defects].

S W Eber; A R Huber

doi:10.1024/0040-5930.63.1.57

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[Red cell membrane defects].

S W Eber·A R Huber

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Abstract

Genetic defects of red cell membrane proteins constitute in Europe the most common cause of congenital hemolytic anemias. During the past decennium the defects and the pathogenetic mechanisms have been eludicated. Relatively simple hematologic tests allow for differentiation into groups with different severity of the disease. This allows prognostic assessment and careful risk-benefit evaluation for splenectomy.

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Anemia, Hemolytic, Congenital Clinical Trials as Topic Erythrocytes, Abnormal Hematologic Tests Humans Practice Guidelines as Topic Practice Patterns, Physicians'Prognosis Risk Assessment Risk Factors Splenectomy English Abstract Journal Article Review

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S W Eber, A R Huber. 2006. [Red cell membrane defects].. https://doi.org/10.1024/0040-5930.63.1.57

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