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PubMed · 1299789

[Micropolyarteritis].

C Dupré-Goudable·C Soler·F Oksman·A Modesto·D Durand·J M Suc
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Abstract

Micropolyarteritis are defined as necrotizing inflammatory lesion of the wall of small vessels affecting different organs. A necrotizing crescentic glomerulonephritis without immuno-deposits is observed in the kidney, frequently involved in this microscopic form of systemic vasculitis. Micropolyarteritis are regrouped with Wegener's syndrome and isolated pauci-immune necrotizing crescentic glomerulonephritis as "ANCA-related vasculitis", whose diagnosis is assessed throw renal biopsy and prognosis dependent on immuno-suppressive treatment. Sixty-one patients treated in our nephrology department for a RPGN during these ten recent years have been retrospectively studied. Among them, twenty-five patients presented clinical and morphologic aspects compatible with the diagnosis of micropolyarteritis. We present their clinical aspects and evolution under treatment.

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Antibodies, Antineutrophil CytoplasmicArteritisAutoantibodiesGlomerulonephritisGranulomatosis with PolyangiitisHumansKidneyEnglish AbstractJournal ArticleReview

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C Dupré-Goudable, C Soler, F Oksman, A Modesto, D Durand, J M Suc. 1992. [Micropolyarteritis].. https://pubmed.ncbi.nlm.nih.gov/1299789/

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