Biomedical subjects
Publications and source records attributed to T Riebel.
A 14 year old Turkish girl presented with unspecific abdominal symptoms and barium enema showed an almost complete obstruction in the region of the splenic flexure. The picture was that of a neoplasm and a left hemicolectomy was performed. Histological examination revealed ulcerating hypertrophic tuberculosis of the colon. The incidence, pathology and symptomatology of colonic tuberculosis are discussed.
The condition of varicocele is rare in childhood. Usually it is not observed before puberty, and can cause infertility if not operated upon in time. With the usual examination of the children in supine position the varicocele can be overlooked. The primary idiopathic type with insufficiency of the spermatic vein is distinguished from the rare secondary symptomatic form, mainly caused by renal tumours. A renal mass should be excluded by an intravenous urography in every case. The percutaneous selective phlebography of the spermatic vein--results in two boys with primary idiopathic varicocele are described--is indicated, if clinical symptoms are still existing despite high ligature of the vein. Further open branches of the spermatic vein and collateral circulation can be shown by this method, the way and type of the second operation better planned, and the patients saved from the threatening infertility.
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The article describes a case of viscerous haemangiomatosis in a 3 1/4-year old girl. Unusually extensive changes in the skin and soft parts, progressing since birth, are shown. Radiological findings for localising visceral haemangiomas are underlined, especially in connection with frequent posthaemorrhagic anaemia as a result of intestinal involvement. Typical x-ray findings: Phleboliths and soft-part "tumours" in plain roentgenograpy (abdomen, soft parts of the skin, cranium); involvement of the walls and disturbances of motility through intestinal haemangiomas in oral and rectal examination with contrast medium; changes in osseous structures and internal organs caused by adjacent angiomatous space-occupying growths.
The symptoms of DeBarsy-Moens-Dierckx-syndrome previously described only in single patients, have been observed in a brother and a sister. Both children showed dwarfism, dystrophy, oligophrenia, an old looking face, and a typically lax skin and cloudy cornea as signs of degeneration of the elastic tissue. Moderate pathological changes were also found in the electroencephalogram, the echoencephalogram, and the X-ray films of the wrists. The analysis of the chromosomes and many other laboratory data were normal. The family-history gave no clue as far as the heredity mode is concerned. As far as we know this is the first description of this syndrome in siblings.
The paper describes the experience gained with tracheobronchography in 11 neonates and young infants with severe pulmonary disease--most of them on artificial respiration--using isotonic solutions of iopromide (17 series) and iotrolan (14 series). Both contrast agents were tolerated without any obvious problems when instilled into the lungs. Because of its higher content of iodine and greater viscosity, iotrolan was superior to iopromide as regards both the demonstration even of the more peripheral bronchial morphology and the duration of the contrast coating.
BACKGROUND: Vasoactive intestinal peptide (VIP) can be produced by mature neurogenic tumors. Pathologically elevated VIP plasma levels cause secretory diarrhea with excessive loss of water and electrolytes. Despite the clinical severity diagnosis of a VIP-secreting tumor is often delayed and subsequently its extirpation as the mainstay of therapy. PATIENTS: We report on two patients with ganglioneuroblastoma and secretory diarrhea. We contrast the case of a 13-month-old boy with advanced symptoms of secretory diarrhea, high VIP plasma levels, and late diagnosis to the case of a 14-month-old boy with mild secretory diarrhea and normal VIP plasma levels but positive proof of VIP in tumor tissue. Reviewing the literature we found 57 cases of pediatric VIP-secreting tumors. RESULTS: The clinical situation is characterized by the typical symptoms of secretory diarrhea with hypokalemia and metabolic acidosis. Histopathology predominantly reveals ganglioneuroblastoma or ganglioneuroma. The symptoms mostly stop after complete resection of the tumor whereas lack of resection is associated with elevated mortality rates. CONCLUSIONS: In case of prolonged therapy-resistant secretory diarrhea the existence of a VIP-secreting tumor should be considered. Diagnostic work-up should include the assessment of VIP plasma levels, catecholamines in urine, and appropriate imaging techniques in order to rule out or confirm the possibility of a VIP producing tumor.
This is a report on the course of a cystic mass in the lower abdomen of a female fetus, which could bei seen by prenatal ultrasound. We are describing differential diagnosis, pre- and postnatal therapy and the origin, as well as the risks of vaginal atresia.