Pulmonary valve atresia with intact ventricular septum. Report of a case with long survival and pulmonary blood supply from an anomalous coronary artery.
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Biomedical subjects
Publications and source records attributed to S C Munsi.
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A 75-year-old male patient presented with resistant congestive cardiac failure. Echocardiographic examination revealed normal left ventricular size with symmetrical hypertrophy and generalised hypokinesia. In addition, there was a characteristic granular sparkling appearance of the myocardium. Cardiac catheterization showed biventricular diastolic restriction with normal coronary arteries. Possibility of cardiac amyloid was considered, and the diagnosis was confirmed on rectal biopsy.
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