[Gallbladder polyps].
There is a relatively high incidence of asymptomatic gallbladder polyps in the general population (1.5-9.5%). We present a 61-year-old woman who had a 22 x 37 mm polyp of the gallbladder.
Female↗
Biomedical subjects
R Reif
Publications and source records attributed to R Reif.
[Desmoid tumors].
Desmoid tumors in various anatomic sites were treated in 4 females and 3 males, ranging in age from 16-50 years, during a 6-year period. In 5 the tumor was completely excised with free margins. In the other 2 excision was incomplete and the tumor recurred within a few months. Desmoid tumors have a marked tendency to local recurrence, and therefore should be widely excised. There is no evidence that adjuvant therapy has a place in the management of these tumors.
Adolescent↗
[Modern ambulatory care of stoma patients].
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Ambulatory Care↗
Intraosseous neurilemmoma of skull--single case report.
Intraosseous neurilemmoma is a rare benign tumour of the bone with characteristic radiological and histological features. The most common places of this tumor are mandible, sacrum and vertebral bodies. A case of a not previously reported location of this tumor in the vault of the skull is presented.
Biopsy↗
[Presystolic increasing maximal flow velocity in the intracranial vessels in 3 children with heart failure].
The doppler-sonographic examination of flow velocities in intracerebral arteries is of central importance in the diagnostic evaluation of potential neurologic complications in intensive care patients. Furthermore pulsed Doppler-sonography can assess the hemodynamic consequences of several congenital heart defects (e.g. the ductus arteriosus Botalli). Characteristics of the normal flow profile in the intracranial arteries are the systolic and diastolic forward flow caused by the "Windkessel" function of the aorta. Well known pathologic flow profiles (systolically and diastolically increased flow velocities, diastolically decreased flow velocities and diastolic retrograde flow) occur in neurologic and cardiovascular diseases. We have investigated three children after cardiac surgery, who showed a presystolic increase in the flow velocities, which is clearly different from the flow profiles mentioned above. In our opinion, this abnormal flow pattern is due to a decreased ventricular output in combination with an elevated central venous pressure in these patients.
Aortic Valve Stenosis↗
Early pyeloplasty for idiopathic hydronephrosis.
Evaluation has been made of a total of 272 patients who underwent surgery for hydronephrosis at the Department of Urology, Faculty Hospital in Olomouc, from 1979 to 1983. On the whole 221 (81%) pyeloplasties and 51 (19%) nephrectomies were performed. Five grades of hydronephrotic nephropathy were distinguished according to their significance. The clinical evaluation was based mainly on the results of excretory urography. The five grades of hydronephrosis were also characterized on the basis of the histological and electron-microscopical patterns and perioperational bioptic findings. Besides the dystrophic changes, seen on the tubular system of the kidney were morphological signs of regeneration, viz. the incidence of differentiated, pale "regeneration cells". However, in advanced stages of hydronephrosis, also these cells are subject to dystrophy making the hydronephrotic changes in the kidney irreversible. On the basis of the histological and clinical findings in correlation with the results of pyeloplasty the authors recommend to operate upon patients with Grades I-II hydronephrosis.
Adolescent↗
[Faulty origin of the right subclavian artery from the pulmonary artery: a rare cause of subclavian steal syndrome in childhood].
A congenital subclavian steal syndrome may be caused by coarctation or interruption of the aortic isthmus or by isolation of a subclavian artery. We describe a patient with D-transposition of the great arteries, a left aortic arch, and isolation of the right subclavian artery which originated from the right pulmonary artery via a right ductus arteriosus. A subclavian steal syndrome was demonstrated noninvasively by echocardiography and doppler sonography of the cerebral arteries. We recommend routine cerebral doppler sonography for all infants with congenital heart disease and unilaterally weak brachial pulses. Since the long term outcome of the congenital subclavian steal syndrome is uncertain the aberrant subclavian artery should be reimplanted at the time of corrective cardiac surgery.
Angiocardiography↗
[Liposarcoma].
During a 12-year period, 10 men and 5 women ranging in age from 22-76 (mean 53 years), were treated for liposarcoma. In 7 the tumor was located in the retroperitoneum, in 5 in the lower extremity and in 1 each, in the back, shoulder and groin. The best results were given by wide excision of the tumor followed by chemo or radiotherapy.
Adult↗
[Personal experience with the treatment of priapism].
The authors discuss the aetiology and therapy of priapism. They deal in detail with different therapeutic approaches and analyze the results with regard to new pathophysiological findings in a group of 23 patients. They mention possible complications and emphasize the necessity of an urgent approach to the solution of this disease. They decide on treatment after assessment of the type of priapism; as to surgical methods they use puncture fenestration according to Winter, if this does not prove satisfactory then they operate according to Al-Ghorab's method.
Adult↗
[Chronic hemorrhagic pancreatitis in gallbladder polyposis as an initial symptom of metachromatic leukodystrophy].
A 4 1/2 year old boy without previous neurologic disorders developed chronic hemorrhagic pancreatitis and was shown to have polyposis of the gallbladder. Neurologic symptoms emerged at the age of 5 years. The sonographic pattern of an echogenic gallbladder was suspect of metachromatic leukodystrophy. The definitive diagnosis was made by the findings of very low arylsulfatase A activity in the white blood cells and deposits of sulfatides in the stroma of the polyps of the gallbladder.
Cerebroside-Sulfatase↗
Peritoneal encapsulation in childhood. Case report, embryologic analysis, and review of literature.
The first reported case of peritoneal encapsulation causing mechanical small bowel obstruction in a child is described. So far, only seven asymptomatic adult patients with this anomaly have been reported on. The embryogenetic basis is discussed. Methods of operative recognition and surgical management are suggested.
Child↗
Autosomal recessive lipid storage myopathy (probable carnitine deficiency).
Two sisters died at the age of 17 and 19, respectively, of a myopathy with exacerbations and remissions characterised by pain and weakness of muscles which ended fatally with lactic acidosis and respiratory failure. The clinical picture was very similar to that described in some cases of carnitine deficiency and the histochemical finding of many lipid-filled vacuoles in muscle fibres and the electron microscopical findings were identical to those reported in that disease. The finding of affected sisters supports autosomal recessive mode of inheritance.
Adolescent↗
[Duodenal hamartomas causing gastrointestinal bleeding].
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Duodenal Neoplasms↗
Severe lower limb malformation associated with other deformities and death in infancy in two brothers.
Two brothers with severe and rare lower limb malformations but normal upper limbs are described. Both brothers had glans hypospadias and they died in early infancy. In the first brother the limb malformation was a severe deformity of the right foot which was split and of rockerbottom shape with oligosyndactyly. In the second brother the right limb below the knee was more severely deformed while only the toes were involved in the left limb. Details of the clinical and pathological findings are described. The most likely mode of inheritance of this rare syndrome is autosomal recessive or X-linked recessive with variable expressivity.
Abnormalities, Multiple↗
Radiation-induced fibrosarcoma following treatment for breast cancer.
A patient with radiation-induced fibrosarcoma following mastectomy and postoperative radiation for bilateral breast carcinoma is described. Only six such cases have been reported in the literature. In this patient erosion of the axillary artery produced massive hemorrhage, and emergency transthoracic ligation of the subclavian artery caused gangrene of the extremity and empyema and sepsis. Interscapulothoracic amputation not only was life-saving but offered the patient a reasonable chance for long-term survival. Only aggressive surgical management can salvage a patient with radiation-induced sarcoma.
Breast Neoplasms↗
[Massive hemorrhage into the urinary bladder in secondary amyloidosis].
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Amyloidosis↗