A case report on a young man who developed after cranial trauma a typical opsoclonus and neurological symptoms dominated by left sensory hemiparesis of the thalamic type; this deficit affected all sensory modalities and involved the whole of the left side, with disturbances of motility caused by impairment of sensation. A general review of opsoclonus is presented and supported by various neurological tables. The discussion on aetiology takes into account the frequent benign causes (encephalitic syndromes, ataxic forms of poliomyelitis), but also the possibility of serious lesions developing in the cerebellum and cerebrum; and finally there remain a number of cases of unknown aetiology. Clinical observations of opsoclonus are rare, and anatomical data is still less; this is why physiopathological interpretations, the object of interesting discussions, are only reached with wisdom.

Adult↗

PubMed1975

Orbital phlebography in the diagnosis of painful ophthalmoplegia.

Three cases of painful ophthalmoplegia have been described in which symptoms suggesting a tumor of the orbit justified neuroradiological assessment. Phlebography in each case revealed stenosis of the superior ophthalmic vein in its third portion, and non-opicification of the cavernous sinus. Hirtz incidences revealed contralateral cavernous sinus opacification and venous drainage through the coronary sinus. These neuradiological findings helped to differentiate this syndrome from other affections which have similar signs and symptoms.

Adult↗

PubMed1975

[Ocular myopathy and electron microscopy (apropos of 8 cases)].

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Eye↗

PubMed1975

[Familial amyloid neuropathy of Corino Andrade. Ultrastructural study of the peripheral nerve in 2 patients].

The authors describe two typical cases of Portuguese amyloid neuropathy in immigrants. One of the patients had been ill for only a short time while the other's condition had been developing over more than ten years. The first patient's neuropathy was characterized by a perforating ulcer of the foot and loss of sensation. The neurological disorder as well as the effect on general health were much more serious in the second patient. Neuro-muscular biopsy was carried out on each of these patients and revealed excessive endoneural amyloid and very severe lesions of nerve parenchyma mainly secondary to Wallerian degeneration. The results were compared with the few existing ultrastructural studies on the peripheral nerve in amyloid neuropathies.

Adult↗

PubMed1974