In our hyperlipidemia test, the total lipids curve, a plateau without a postprandial peak, allows an easy diagnosis of the chyliferous blockage. The malformation of chyliferous vessels produces the congenital forms: exsudative enteropathy, chyloperitoneum, spontaneous chylothorax, chylous cyst of the mediastinum, reflux of chyle in the pulmonary lymphatics, lymphoedema with chyle reflux in the lymphatics of the leg and chyluria. The acquired forms comprise the post-infectious sclerosis of the intestinal lymphatics and the neoplastic invasions of the mesenteric lymph nodes. The optical density curve brings some informations for a better understanding of lipid's absorption.

Adult↗

PubMedDate not supplied

[Deep vein malformations in the Klippel-Trenaunay syndrome].

Klippel's syndrome is due to a malformation of the deep veins. From 1944 to 1978 we have operated on 614 cases. In 51 % of these cases the malformation concerned the popliteal vein, in 16 % it concerned the superficial femoral vein, and in 25 % both veins were affected. We had only 3 % of iliac malformations and 1 % of inferior vena caval malformation. In the popliteal vein, ageneses and atresias were of equal incidence, but compressions by fibrous bands were much more frequent. In the femoral vein, compressions were most frequent, followed by atresias. Ageneses were very rare. In the iliac vein, atresias were twice as common as ageneses, whereas with the inferior vena cava we only found ageneses. The obstruction to the deep veins can be sectioned but one must also free the supplying vessels.

Angiomatosis↗

PubMedDate not supplied

[Malformations of the lacteals].

For the diagnosis of malformations of the lymphatics is made by the hyperlipidaemia test, which shows a flat total lipids curve without a post-prandial peak. Malformation of the lymphatics of the small intestine is responsible for exudative enteropathy, chyloperitoneum, chyluria, lymphoedema with reflux of lymph in the lymphatics of the legs and its complications (chylorrhagia, chylarthrosis), chylothorax, chylopericardium and reflux of lymph in the pulmonary lymphatics. This malformation can also be associated with other disorders : such as the syndrome of Klippel and Trenaunay, and simple lymphoedema of the limbs or genital organs. Lymphography of the intestinal lymphatics carried out during laparotomy after a fatty meal shows the state of the lymphatic vessels, a lack of injection of the cistern of Pecquet, and above all the presence of adventitious vessels allowing the lymph to reach the cervical region.

Adolescent↗

PubMedDate not supplied

The induced hyperlipemia test.

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Adult↗

PubMedDate not supplied

Spontaneous, post-operative and traumatic chylothorax.

Study of the malformation of the chyliferous vessels, malformations of Pecquet's cistern or of the thoracic duct has brought out the nature of the physiopathology of spontaneous chylothorax: it is the result of a rupture of a lymphatic of the diaphragm, mediastinum, or lung. Post-operative chylothorax is due to a lesion of the thoracic duct or of one of its branches.

Adult↗

PubMedDate not supplied

[Circulating antiprothrombinase anticoagulant, thrombosis and spontaneous abortions; a new syndrome].

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Abortion, Habitual↗