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Biomedical subjects

M Ribierre

Publications and source records attributed to M Ribierre.

At least 19 recordsLinked to original sources
PubMed1987

[Mitral atresia. Anatomical aspects].

This study is devoted to a series of 30 anatomical cases of mitral atresia. The left atrium was dilated in 5 cases and hypoplastic in 25. The interatrial ostium was small in 50% of the hearts. Left atrio-ventricular concordance was present in 29 cases, as against 1 case of discordance. There was no atrio-ventricular connection in 29 cases, and the mitral valve was imperforate in 1 case. Connections between the tricuspid valve and the main ventricle were normal in 26 hearts. The tricuspid valve straddled the septum in 4 cases. Five hearts had two ventricles, 25 had a single ventricle. Nine hearts showed no ventriculo-atrial atresia. The main vessels were normally located in 1 case, transposed in 2 and originated in the right ventricle in 2 cases; in the 5 hearts with single ventricle the two main vessels arose from the main cavity. Seventeen hearts had an atresic aortic valve and a hypoplastic ascending aorta; the pulmonary artery arose from the right ventricle in 1 case and from the main chamber of a single ventricle heart in 15 cases. The pulmonary valve was atresic and the aorta arose from the main chamber of a single ventricle heart in 4 cases.

Aortic Valve↗
PubMed1986

Double outlet right ventricle associated with common atrioventricular canal: report of nine anatomic specimens.

Double outlet right ventricle associated with complete atrioventricular (AV) canal is a rare malformation. Nine cases are reported. In this abnormality the anterior AV leaflet is undivided and free floating and the aortic and pulmonary orifices are in the same frontal plane. In four of the nine cases, the conus was bilateral, but it was slightly hypoplastic in two. In five cases there was no subaortic conus and there was mitral-aortic continuity through the ventricular septal defect. Pulmonary stenosis was present in eight cases. Radiograms may best demonstrate the anatomy of the ventricular septal defect; it extends far anteriorly below the aortic valve, and its inferior rim is deviated by the trabecula septomarginalis.

Heart Defects, Congenital↗
PubMed1984

[Pseudoxanthoma elasticum with aortic insufficiency and arterial hypertension in a 12-year-old boy].

Hypertension was found in a 12 year-old Tunisian boy in the weeks following an aortic valvular replacement for aortic regurgitation which was surmised to be rheumatic in origin. In fact, the hypertension and aortic regurgitation were due to the Gröenblad-Strandberg syndrome, or pseudoxanthoma elasticum. The origin of the hypertension was demonstrated by selective renal angiography which showed interruption of the distal cortical renal arteries. Deposition of calcium in the arterial wall was shown by renal ultrasonography. The origin of aortic regurgitation was first imputed to acute rheumatic fever. Thus, the patient presented with complete picture of pseudoxanthoma elasticum with skin, arterial and cardiac involvement. The case reported is the third with a cardiac involvement. The case reported is the third with a cardiac localization of the disease histologically proven in a patient under 20 years of age. The frequency, transmission, histologic findings, etiopathogenesis and clinical aspects of pseudoxanthoma elasticum are reviewed in brief.

Aortic Valve Insufficiency↗
PubMed1982

[Acute infectious myocarditis (author's transl)].

Among the primary myocardiopathies resulting from a known cause, acute infectious myocarditis plays an important part. This condition, usually interstitial myocarditis of viral etiology, occurs predominantly in the infant under two years of age. They are characterized by a hypotrophic hypokinetic myocardiopathy which is very hard to differentiate from endocardial fibroelastosis. Fibroelastosis is probably only one possible result of the course of certain myocarditis'. However, on the whole, prognosis is good and the children recover. Typhoid fever and diphtheria may also compromise myocardial function.

Acute Disease↗
PubMed1979

[Therapeutic embolization of a congenital vertebral arteriovenous fistula].

An arterio-venous fistula in the neck arising from the right vertebral artery is described. Selective angiography showed a single communication. A Fogarty catheter, introduced by the occipital artery and left in situ was used as a means of embolisation. This procedure was simple and effective.

Arteriovenous Malformations↗
PubMed1978

[Apparently primary acute heart failure in infants. Long-term outcome].

Cases of acute cardiac failure which are apparently primary, and occurring in babies or young children have one characteristics clinical picture. There are three etiological agents, which cannot be differentiated clinically: myocarditis, fibroelastosis, and primary non-obstructive cardiomyopathies. When the critical early period, which still carries a high mortality, has been passed, the outlook is relatively favourable. 61 babies or infants of less than 30 months with acute primary cardiac failure were followed up for a period of between 5 and 20 years. 33 of them were considered cured; 22 have minor sequelae (most frequently) left ventricular hypertrophy on X-ray or ECG); 3 have persistent cardiac failure despite treatment; 3 have died after a period of more than 5 years. There is no clinical, X-ray or ECG finding which can predict the longterm outlook in this condition. It is virtually impossible to differentiate between myocarditis and firboelastosis; it seems likely in the majority of cases that we are dealing with different modes of development in the same condition.

Cardiomyopathies↗