The pathogenesis of the phacomatoses, developmental diseases of the embryonic plates, permits an understanding of the different manifestations which characterize these disorders. This pathogenesis also constitutes the best basis for a rational classification. The author sets out the main features of this pathogenesis and its practical applications, and then considers the principal vascular aspects of the phacomatoses, especially in Osler-Rendu disease, Blue Rubber Bleb Naevi, Mafussi's syndrome, the haemangioblastomatoses, Bailey's glomangiomatosis, the Louis-Bar syndrome, Struge-Weber angiomatosis, the syndrome of Bonnet-Dechaume and Blanc, Cobb's syndrome, the angio-osteo-hypertrophic syndromes, von Recklinghausen's neurofibromatosis, Bourneville's tuberous sclerosis, and the melanic phacomatoses.

Adolescent↗

PubMedDate not supplied

[Radical surgery for a multipedunculated vertebral fistula by a combined sequential endo- and exovascular approach (author's transl)].

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Adult↗

PubMedDate not supplied

[Large ethmoido-frontal mucocoele with exorbitism; amaurosis and displacement of the dura mater. The value of the scanner. Treatment by marsupialisation into th nasal fossa (author's transl)].

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Blindness↗

PubMedDate not supplied

Aneurysm associated with a fenestrated basilar artery: report of two cases treated by endovascular detachable balloon embolization.

The authors report two cases of aneurysms originating at a fenestration of the basilar artery treated by endovascular placement of a balloon inside the aneurysm with preservation of the patent vessel.

Adult↗

PubMedDate not supplied

[Indications for the use of thrombolytics in cases of cerebrovascular thrombosis also treated with hyperbaric oxygenation (2 ATA)].

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Adult↗