Surgical correction of Ebstein's anomaly.
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Biomedical subjects
Publications and source records attributed to J Somerville.
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Two children with unobstructed total anomalous pulmonary venous drainage and hyperkinetic pulmonary hypertension deteriorated with pulmonary oedema and cerebral symptoms following angiocardiography using large amounts of contrast medium. One patient died. The dangers of this with resultant hypernatraemia are discussed.
Based on experience with 48 patients, a new simple classification of pulmonary atresia, according to pulmonary artery development is suggested. The need for extensive investigation including biplane aortography and right ventricular angiocardiography is emphasized. Adequate display of the anatomy is required to plan the surgical management. Early palliative procedures are advised for hypoxia and later radical correction is possible in a large number of these patients.
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