[A case of demyelinating disease with acute transverse myelitis and polyradiculoneuropathy (author's transl)].
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Acute Disease↗
Biomedical subjects
H Nogaki
Publications and source records attributed to H Nogaki.
Rigid spine syndrome associated with cardiomyopathy: clinical and nosological considerations.
We report observations in a 32-year-old man with the following characteristics of rigid spine syndrome: humero-peroneal muscular atrophy and weakness; bradycardia, dilated cardiomegaly and complete cardiac conduction block; and severe fatty degeneration of the paravertebral and calf muscles. The latter showed a predominance of type 1 fibers, a deficiency of type 2A fibers, and an increase in type 2C fibers. The patient had no familial background of the disease. There was no contracture of the elbows. These findings, especially the severe cardiac involvement, suggest that the rigid spine syndrome can be difficult to distinguish from the Emery-Dreifuss form of muscular dystrophy.
Adult↗
Systemic lupus erythematosus associated with marked intracranial calcification.
The authors describe a case of systemic lupus erythematosus associated with marked intracerebral calcification. The distribution of high signal on T1-weighted MR images was almost identical to the distribution of calcification on CT; however, the bodies of caudate nuclei with little calcification on CT also showed high intensities on T1-weighted images.
Adult↗