Compensation of chain synthesis by the single chain gene in Hb Lepore trait.
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Biomedical subjects
Publications and source records attributed to H Lehmann.
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Two Ghanaian women with sickle-cell anaemia and alpha-thalassaemia were found to have an unusually benign obstetric history. In addition to two factors present which are known to moderate the clinical course of sickle-cell anaemia, good socioeconomic status and a relatively high Hb F level, it is suggested that alpha-thalassaemia may act among other things by lowering the haemoglobin concentration in the red cells and thereby lowering their tendency to sickle in vivo.
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