[Malabsorption syndrome and intestinal pseudoobstruction in primary vascular and heart amyloidosis].
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Biomedical subjects
Publications and source records attributed to H J Schulz.
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Description is given of two sisters, offspring of a first cousin marriage, who exhibited the following identical lesions: 1) cysts of the borders of upper and lower lids; 2) hypodontia; 3) hypotrichosis; 4) palmo-plantar keratosis and 5) onychodystrophy. It is suggested that this combination represents a previously unrecognized autosomal recessive trait in man.
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