Development of myelin in inherited disorders of amino acid metabolism.
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Adolescent↗
Biomedical subjects
A L Prensky
Publications and source records attributed to A L Prensky.
Clinical and electroencephalographic manifestations of vascular lesions of the pons.
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Adult↗
Biochemical and histochemical studies of a case of Farber's lipogranulomatosis.
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Gangliosides↗
Further observations on the biochemical lesion in maple syrup urine disease.
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Animals↗
Intravenous diazepam in the treatment of prolonged seizure activity.
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Adolescent↗
The relationship of biochemical and morphological information in the central nervous system: the problem of sampling.
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Brain↗
Changes in the amino acid composition of proteolipids of white matter during maturation of the human nervous system.
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Adult↗
Brain lipids, proteolipids, and free amino acids in maple syrup urine disease.
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Amino Acids↗
The moyamoya syndrome associated with irradiation of an optic glioma in children: report of two cases and review of the literature.
We report two cases of the moyamoya syndrome which became clinically apparent after irradiation of an optic glioma during childhood. A summary of 14 cases of this syndrome following irradiation of intracranial tumors is also presented. Nine of these cases were optic gliomas; five were found in children with neurofibromatosis, another disorder that has a strong association with the moyamoya syndrome. The effectiveness of irradiation of optic gliomas in childhood is not definitely established. The possibility of inducing serious vascular disease is a further reason for caution when considering irradiating these tumors.
Arterial Occlusive Diseases↗